ICD-11 classes
08 Diseases of the nervous system
Multiple sclerosis or other white matter disorders
8A44 — Leukodystrophies
8A44.0 — Pelizaeus-Merzbacher disease
LD90.2 — Pelizaeus-Merzbacher-like disease

ICD-11 LD90.2 — Pelizaeus-Merzbacher-like disease

Pelizaeus-Merzbacher like disease (PMLD) is an autosomal recessive leukodystrophy sharing identical clinical and radiological features as X-linked Pelizaeus-Merzbacher disease (PMD; ).

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Conditions with disorders of intellectual development as a relevant clinical feature #23735
• Pelizaeus-Merzbacher disease #23743