ICD-11 classes
08 Diseases of the nervous system
Multiple sclerosis or other white matter disorders
8A45 — Secondary white matter disorders
8A45.4 — White matter disorders due to certain specified systemic...
8A45.44 — Demyelination due to systemic vasculitis

ICD-11 8A45.44 — Demyelination due to systemic vasculitis

The CNS vasculature can be targeted by systemic vasculitis and include the following conditions; Small-Medium Vessel Vasculitis — Wegener’s granulomatosis, microscopic polyangiitis, Churg-Strauss syndrome, Cryoglobulinemic vasculitis and Behçet’s disease.Medium Vessel Vasculitis — Polyarteritis nodosa Large Vessel Vasculitis — Giant-cell arteritis, Takayasu’s arteritis (Neurologic complications are mainly due to involvement of extracranial vessels). Usually CNS involvement coexists with other clearly apparent systemic manifestations but some patients may present primarily with prominent symptoms of CNS dysfunction

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

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