ICD-11 classes
08 Diseases of the nervous system
Epilepsy or seizures
8A61 — Genetic or presumed genetic syndromes primarily expressed...
8A61.2 — Genetic epileptic syndromes with childhood onset
8A61.23 — Myoclonic absences or absences with myoclonias

ICD-11 8A61.23 — Myoclonic absences or absences with myoclonias

Childhood epileptic syndrome characterised by absence seizures associated with severe rhythmic bilateral myoclonic jerks. The EEG pattern shows rhythmic, bilateral, synchronous, symmetric 3-Hz spike and slow-waves discharges associated with EMG myoclonic bursts at 3 Hz, superimposed to a progressively increasing tonic contraction.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.