ICD-11 classes
08 Diseases of the nervous system
Epilepsy or seizures
8A62 — Epileptic encephalopathies
8A62.0 — Infantile spasms
ICD-11 8A62.0 — Infantile spasms
Syndrome characterised by the subacute onset of brief, repeated seizures with axial or limb flexion, occurring in clusters. EEG shows hypsarrhythmia, i.e., chaotic, high voltage slowing multifocal spikes, with ictal abrupt decremental pattern. Various structural brain pathologies may be present, or no cause may be found. Two-thirds of children have subsequent cognitive deficits.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.