ICD-11 classes
08 Diseases of the nervous system
Spinal cord disorders excluding trauma
8B41 — Myelitis
8A43 — Neuromyelitis optica
8A43.0 — Neuromyelitis optica aquaporin-4 antibody positive

ICD-11 8A43.0 — Neuromyelitis optica aquaporin-4 antibody positive

Neuromyelitis optica (NMO) is an inflammatory demyelinating disease of the central nervous system characterised mainly by attacks of uni- or bilateral optic neuritis (ON) and acute longitudinally extensive (> 3 vertebral segments) myelitis. This form is seropositive for aquaporin-4 antibodies.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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