ICD-11 classes
08 Diseases of the nervous system
Motor neuron diseases or related disorders
8B60 — Motor neuron disease
8B60.3 — Progressive muscular atrophy
ICD-11 8B60.3 — Progressive muscular atrophy
In progressive muscular atrophy, lower motor neuron signs in limb and trunk muscles are present without upper motor neuron involvement. Over time, some patients may progress to develop upper motor neuron signs, of which pathological evidence is common even in patients who never displayed clinical upper motor neuron signs, suggesting that progressive muscular atrophy is a form of ALS.
The diagnosis includes nothing.
It excludes 2 items.
- Fazio-Londe syndrome (8B60)
- Amyotrophic lateral sclerosis (8B60.0)
It has no clarifying diagnoses.