ICD-11 classes
08 Diseases of the nervous system
Motor neuron diseases or related disorders
8B60 — Motor neuron disease
8B60.6 — Monomelic amyotrophy

ICD-11 8B60.6 — Monomelic amyotrophy

Atrophy and weakness restricted to one upper or lower limb, onset in the second or third decade, male predominance, and sporadic occurrence are characteristic features of MMA. Other typical features include: insidious onset of lower motor neuron signs due to anterior horn cell involvement, absence of upper motor neuron signs, slow progression followed by stabilization within a few years, and a benign symptomatic disease course. MMA is particularly prevalent in Asia although is encountered worldwide.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.