ICD-11 classes
08 Diseases of the nervous system
Disorders of nerve root, plexus or peripheral nerves
Disorders of cranial nerves
8B81 — Disorders of vestibulocochlear nerve
AB31 — Episodic vestibular syndrome
AB31.5 — Autoimmune inner ear disease

ICD-11 AB31.5 — Autoimmune inner ear disease

Autoimmune inner ear disease (AIED) is a clinical syndrome of bilateral sensorineural hearing loss (SNHL) >30dB at one or more frequencies progressing over a period of 3-90 days. Progression of SNLH >15dB at one frequency or >10dB in two frequencies in at least one ear should be demonstrated. Vestibular symptoms may be present in 50% of patients and systemic autoimmune disease (SAD) coexists in 30% of patients.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Episodic vestibular syndrome #10679