ICD-11 classes
08 Diseases of the nervous system
Disorders of nerve root, plexus or peripheral nerves
9C40 — Disorder of the optic nerve
9C40.B — Optic atrophy

ICD-11 9C40.B — Optic atrophy

Optic atrophies (OA) refer to a specific group of hereditary optic neuropathies in which the cause of the optic nerve dysfunction is inherited either in an autosomal dominant or autosomal recessive pattern. Autosomal dominant optic atrophy (ADOA), type Kjer, is the most common OA, whereas autosomal recessive optic atrophy (AROA) is a rare form.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 9C40.B contains 3 clarifying diagnoses:

1. 9C40.B0 — Congenital optic atrophy
2. 9C40.B1 — Acquired optic atrophy
3. 9C40.BZ — Optic atrophy, unspecified

The diagnosis is coded elsewhere:

• Disorder of the optic nerve #9776
• Optic atrophy #9809