ICD-11 classes
08 Diseases of the nervous system
Diseases of neuromuscular junction or muscle
Secondary myopathies
8C81 — Autoimmune myopathy
ICD-11 8C81 — Autoimmune myopathy
Autoimmune myopathy is a subgroup of idiopathic inflammatory myopathies, which despite diverse causes, have the common histopathological features of myocyte necrosis without significant inflammation. Patients present with a subacute severe symmetrical proximal myopathy, associated with a markedly elevated creatine kinase level. These are most likely immune-mediated, as they respond to immunotherapy. it is often accompanied by statin therapy, connective tissue diseases, cancer, and autoantibodies specific for signal recognition particle (SRP) or 3-hydroxy-3-methylglutaryl–coenzyme A reductase (HMGCR).
The diagnosis includes nothing.
It excludes 2 items.
- Myasthenia gravis or certain specified neuromuscular junction disorders (8C60-8C6Z)
- Primary disorders of muscles (8C70-8C7Z)
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Secondary myopathies #10091