ICD-11 classes
08 Diseases of the nervous system
Disorders of autonomic nervous system
8D87 — Autonomic nervous system disorder due to certain specified...
8D87.0 — Multiple system atrophy
8D87.01 — Multiple system atrophy, Parkinsonism

ICD-11 8D87.01 — Multiple system atrophy, Parkinsonism

This is a progressive disorder of the central and autonomic nervous systems, characterised by orthostatic hypotension (an excessive drop in blood pressure when standing up), which causes dizziness or fainting. It can occur without orthostatic hypotension, but instead have urinary involvement (urgency/incontinence). This type includes symptoms of Parkinson's disease such as slow movement, rigidity, and tremor.

The diagnosis includes nothing.

It excludes 2 items.

  • Spinocerebellar ataxia (8A03.16)
  • Pure autonomic nervous system failure (8D84)

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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