ICD-11 classes
08 Diseases of the nervous system
Human prion diseases
8E00 — Sporadic Creutzfeldt-Jakob Disease
ICD-11 8E00 — Sporadic Creutzfeldt-Jakob Disease
A disease of the brain, that is associated with a mutation of normal prion protein genes or spontaneous transformation of prion proteins. This disease is characterised by a long incubation period, progressive dementia, neurological deficits, and is fatal. Transmission may be by direct contact with infected nervous tissue or blood. Confirmation is by pathological examination of the brain.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Human prion diseases #1434