ICD-11 classes
08 Diseases of the nervous system
Structural developmental anomalies of the nervous system
LA00 — Anencephaly or similar anomalies

ICD-11 LA00 — Anencephaly or similar anomalies

A malformation of the nervous system caused by the failure of neuropore closure. Infants are born with intact spinal cord, cerebellum, and brainstem, but lack formation of neural structures above this level. The skull is only partially formed but the eyes are usually normal.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code LA00 contains 6 clarifying diagnoses:

1. LA00.0 — Anencephaly
   It contains 3 clarifying diagnoses.
2. LA00.1 — Iniencephaly
3. LA00.2 — Acephaly
4. LA00.3 — Amyelencephaly
5. LA00.Y — Other specified anencephaly or similar anomalies
6. LA00.Z — Anencephaly or similar anomalies, unspecified

The diagnosis is coded elsewhere:

• Structural developmental anomalies of the nervous system #22217
• Anencephaly or similar anomalies #22218