ICD-11 classes
08 Diseases of the nervous system
Structural developmental anomalies of the nervous system
LA04 — Congenital hydrocephalus
ICD-11 LA04 — Congenital hydrocephalus
A disease caused by failure of the brain to correctly develop during the antenatal period. This condition is characterised by a rapid increase in head circumference or an unusually large head size due to excessive accumulation of cerebrospinal fluid in the brain. This condition may also present with vomiting, sleepiness, irritability, downward deviation of the eyes, or seizures. Confirmation is through observation of cerebrospinal fluid within cerebral ventricles by imaging.
It includes 1 item.
- Hydrocephalus in newborn
It excludes 4 items.
- Myelomeningocele with hydrocephalus (LA02.00)
- Hydrocephalus due to congenital toxoplasmosis (KA64.0)
- Arnold-Chiari malformation type I (LA07.4)
- Arnold-Chiari malformation type II (LA03)
Diagnosis with code LA04 contains 3 clarifying diagnoses:
- LA04.0 — Hydrocephalus with stenosis of the aqueduct of Sylvius
- LA04.Y — Other specified congenital hydrocephalus
- LA04.Z — Congenital hydrocephalus, unspecified
The diagnosis is coded elsewhere:
- Neonatal hydrocephalus #7628
- Congenital hydrocephalus #7630
- Neonatal hydrocephalus #21893
- Congenital hydrocephalus #21895
- Structural developmental anomalies of the nervous system #22217
- Congenital hydrocephalus #22240