ICD-11 classes
09 Diseases of the visual system
Disorders of the eyeball - posterior segment
Disorders of the retina
9B78 — Certain specified retinal disorders
9B78.0 — Retinal vasculopathy and cerebral leukodystrophy

ICD-11 9B78.0 — Retinal vasculopathy and cerebral leukodystrophy

Retinal vasculopathy and cerebral leukodystrophy is an inherited group of small vessel diseases comprised of cerebroretinal vasculopathy, hereditary vascular retinopathy and hereditary endotheliopathy with retinopathy, nephropathy and stroke (HERNS); all exhibiting progressive visual impairment as well as variable cerebral dysfunction.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.