ICD-11 classes
09 Diseases of the visual system
Strabismus or ocular motility disorders
Diseases of neuromuscular junction or muscle
Primary disorders of muscles
4A41 — Idiopathic inflammatory myopathy
4A41.0 — Dermatomyositis
4A41.00 — Adult dermatomyositis

ICD-11 4A41.00 — Adult dermatomyositis

Adult dermatomyositis is a systemic inflammatory disorders affecting the skeletal muscles, the skin, and other organs. It is characterised by symmetric proximal muscle weakness, increased serum muscle enzymes, myopathic changes upon electromyography, typical histological findings on muscle biopsy, and typical dermatologic manifestations such as heliotrope rash or Gottron’s papules.

The diagnosis includes nothing.

It excludes 1 item.

  • Myasthenia gravis or certain specified neuromuscular junction disorders (8C60-8C6Z)

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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