ICD-11 classes
11 Diseases of the circulatory system
Neoplasms of the circulatory system
Malignant mesenchymal neoplasms

ICD-11 Malignant mesenchymal neoplasms

A usually aggressive malignant mesenchymal cell tumour most commonly arising from muscle, fat, fibrous tissue, bone, cartilage, and blood vessels. Sarcomas occur in both children and adults. The prognosis depends largely on the degree of differentiation (grade) of the tumour. Representative subtypes are liposarcoma, leiomyosarcoma, osteosarcoma, and chondrosarcoma.

The diagnosis includes nothing.

Diagnosis contains 22 clarifying diagnoses:

1. 2B50 — Chondrosarcoma, primary site
   It contains 5 clarifying diagnoses.
2. 2B51 — Osteosarcoma, primary site
   It contains 5 clarifying diagnoses.
3. 2B52 — Ewing sarcoma, primary site
   It contains 6 clarifying diagnoses.
4. 2B53 — Fibroblastic or myofibroblastic tumour, primary site
   It contains 4 clarifying diagnoses.
5. 2B54 — Unclassified pleomorphic sarcoma, primary site
   It contains 4 clarifying diagnoses.
6. 2B55 — Rhabdomyosarcoma, primary site
   It contains 5 clarifying diagnoses.
7. 2B56 — Angiosarcoma, primary site
   It contains 6 clarifying diagnoses.
8. 2B57 — Kaposi sarcoma, primary site
   It contains 5 clarifying diagnoses.
9. 2B58 — Leiomyosarcoma, primary site
   It contains 5 clarifying diagnoses.
10. 2B59 — Liposarcoma, primary site
    It contains 5 clarifying diagnoses.
11. 2B5A — Synovial sarcoma, primary site
    It contains 4 clarifying diagnoses.
12. 2B5B — Gastrointestinal stromal tumour, primary site
    It contains 4 clarifying diagnoses.
13. 2B5C — Endometrial stromal sarcoma, primary site
14. 2B5D — Malignant mixed epithelial mesenchymal tumour, primary site
    It contains 4 clarifying diagnoses.
15. 2B5E — Malignant nerve sheath tumour of peripheral nerves or autonomic nervous system, primary site
16. 2B5F — Sarcoma, not elsewhere classified, primary site
    It contains 4 clarifying diagnoses.
17. 2B5G — Myosarcoma of uterus, part not specified
    It contains 1 clarifying diagnosis.
18. 2B5H — Well differentiated lipomatous tumour, primary site
19. 2B5J — Malignant miscellaneous tumours of bone or articular cartilage of other or unspecified sites
20. 2B5K — Unspecified malignant soft tissue tumours or sarcomas of bone or articular cartilage of other or unspecified sites
21. 2B5Y — Other specified malignant mesenchymal neoplasms
22. 2B5Z — Malignant mesenchymal neoplasm of unspecified type

The diagnosis is coded elsewhere:

• Malignant neoplasms, stated or presumed to be primary, of specified sites, except of lymphoid, haematopoietic, central nervous system or related tissues #1778
• Malignant mesenchymal neoplasms #1779
• Neoplasms of the musculoskeletal system #18234
• Malignant mesenchymal neoplasms #18235