ICD-11 classes
11 Diseases of the circulatory system
Neoplasms of the circulatory system
Malignant mesenchymal neoplasms
2B54 — Unclassified pleomorphic sarcoma, primary site

ICD-11 2B54 — Unclassified pleomorphic sarcoma, primary site

A pleomorphic sarcoma characterised by the presence of fibrohistiocytic cells and spindle cells arranged in a storiform pattern.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 2B54 contains 4 clarifying diagnoses:

  1. 2B54.0 — Unclassified pleomorphic sarcoma of skin
  2. 2B54.1 — Unclassified pleomorphic sarcoma of retroperitoneum or peritoneum
  3. 2B54.Y — Unclassified pleomorphic sarcoma, primary site, other specified site
  4. 2B54.Z — Unclassified pleomorphic sarcoma, primary site, unspecified site

The diagnosis is coded elsewhere:

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