ICD-11 classes
11 Diseases of the circulatory system
Neoplasms of the circulatory system
Malignant mesenchymal neoplasms
2B52 — Ewing sarcoma, primary site
2B52.3 — Ewing sarcoma of soft tissue
ICD-11 2B52.3 — Ewing sarcoma of soft tissue
A rare malignant neoplasm of the soft tissues. It is typically a disease of children and young adults. It is characterised by t(11:22) (q24: q12) resulting in the expression of EWS/FLI-1 chimeric transcript. Most commonly occurs in the paravertebral region, chest wall, pelvis and lower extremities.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Ewing sarcoma, primary site #1792
- Ewing sarcoma, primary site #18248