ICD-11 classes
11 Diseases of the circulatory system
Neoplasms of the circulatory system
Malignant mesenchymal neoplasms
2B56 — Angiosarcoma, primary site
2B56.1 — Angiosarcoma of skin
ICD-11 2B56.1 — Angiosarcoma of skin
A malignant tumour arising from the endothelial cells of the blood vessels. Microscopically, it is characterised by frequently open vascular anastomosing and branching channels. The malignant cells that line the vascular channels are spindle or epithelioid and often display hyperchromatic nuclei. Angiosarcomas most frequently occur in the skin and breast. Patients with long-standing lymphoedema are at increased risk of developing angiosarcoma.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Angiosarcoma, primary site #1815
- Cutaneous sarcoma #2198
- Cutaneous sarcoma #17536
- Angiosarcoma, primary site #18271