ICD-11 classes
11 Diseases of the circulatory system
Developmental anomalies of the circulatory system
Structural developmental anomalies of the circulatory system
Structural developmental anomaly of heart or great vessels
LA87 — Congenital anomaly of an atrioventricular valve or...
LA87.0 — Congenital anomaly of tricuspid valve
LA87.03 — Ebstein malformation of tricuspid valve
ICD-11 LA87.03 — Ebstein malformation of tricuspid valve
A congenital cardiovascular malformation of the tricuspid valve and right ventricle that is characterised by incomplete delamination of the septal and inferior (posterior) tricuspid valvar leaflets from the myocardium of the right ventricle, and varying degrees of downward (apical) rotational displacement of the functional annulus.Additional information: associated cardiac anomalies include an interatrial communication, the presence of accessory conduction pathways and varying degrees of right ventricular outflow tract obstruction, including pulmonary atresia. In the setting of discordant atrioventricular and ventriculo-arterial connections ['Congenitally corrected transposition of great arteries'], 'Ebstein malformation of tricuspid valve' may be present.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: