ICD-11 classes
11 Diseases of the circulatory system
Developmental anomalies of the circulatory system
Structural developmental anomalies of the circulatory system
Structural developmental anomaly of heart or great vessels
LA89 — Functionally univentricular heart
LA89.3 — Hypoplastic left heart syndrome
ICD-11 LA89.3 — Hypoplastic left heart syndrome
A spectrum of congenital cardiovascular malformations with normally aligned great arteries without a common atrioventricular junction, characterised by underdevelopment of the left heart with significant hypoplasia of the left ventricle including atresia, stenosis, or hypoplasia of the aortic or mitral valve, or both valves, and hypoplasia of the ascending aorta and aortic arch.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: