ICD-11 classes
11 Diseases of the circulatory system
Developmental anomalies of the circulatory system
Structural developmental anomalies of the circulatory system
Structural developmental anomaly of heart or great vessels
LA8A — Congenital anomaly of a ventriculo-arterial valve or...
LA8A.3 — Congenital supravalvar aortic stenosis

ICD-11 LA8A.3 — Congenital supravalvar aortic stenosis

A congenital cardiovascular malformation with narrowing of the aorta at the level of the sinotubular junction which may extend into the ascending aorta.Additional information: 'Congenital supravalvar aortic stenosis' is described as three forms: an hourglass deformity, a fibrous membrane, and a diffuse narrowing of the ascending aorta. Supravalvar aortic stenosis may involve the coronary artery ostia, and the aortic leaflets may be tethered. The coronary arteries can become tortuous and dilated due to elevated pressures and early atherosclerosis may ensue.

The diagnosis includes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Congenital anomaly of a ventriculo-arterial valve or adjacent regions #22613