ICD-11 classes
12 Diseases of the respiratory system
Pleural, diaphragm or mediastinal disorders
CB22 — Diseases of mediastinum, not elsewhere classified
CB22.0 — Fibrosing mediastinitis

ICD-11 CB22.0 — Fibrosing mediastinitis

Fibrosing mediastinitis, also known as sclerosing mediastinitis or mediastinal fibrosis, is a disorder characterised by an excessive fibrotic reaction in the mediastinum. It can result in compromise of airways, great vessels, and other mediastinal structures, with morbidity directly related to the location and extent of fibrosis. The commonest cause is histoplasmosis, of which it is a rare late complication, but it may also occur in association with other infections and with systemic autoimmune disorders such as Behçet disease, granulomatosis with polyangiitis and retroperitoneal fibrosis.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.