ICD-11 classes
13 Diseases of the digestive system
Diseases or disorders of orofacial complex
DA01 — Disorders of oral mucosa
DA01.1 — Noninfectious erosive or ulcerative disorders of oral mucosa
EB13.0 — Stevens-Johnson syndrome
ICD-11 EB13.0 — Stevens-Johnson syndrome
Stevens-Johnson syndrome is an immune-complex–mediated hypersensitivity disorder involving mucous membranes (conjunctivae, oral mucosa and genital mucosa) with, by definition, skin involvement limited to no more than 9% body surface area. It is related to toxic epidermal necrolysis and shares many of the same triggers, notably drugs, but the inflammation is centred on and close to mucosal surfaces. Although mortality is low, acute morbidity is high and conjunctival involvement has the potential to cause blindness.
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code EB13.0 contains 1 clarifying diagnosis:
The diagnosis is coded elsewhere:
- Stevens-Johnson syndrome or toxic epidermal necrolysis #15761
- Noninfectious erosive or ulcerative disorders of oral mucosa #16830
The diagnosis is included in 3 other classes.
- Drug-induced Stevens-Johnson syndrome (EH63.0)
- Acute cicatrizing conjunctivitis, Stevens-Johnson's (9A60.2)
- Chronic cicatrizing conjunctivitis, Stevens-Johnson's (9A60.2)