ICD-11 classes
14 Diseases of the skin
Inflammatory dermatoses
Inflammatory erythemas and other reactive inflammatory...
EB13 — Stevens-Johnson syndrome or toxic epidermal necrolysis

ICD-11 EB13 — Stevens-Johnson syndrome or toxic epidermal necrolysis

A spectrum of severe and life-threatening hypersensitivity disorders affecting skin and mucous membranes, most commonly precipitated by an idiosyncratic reaction to medication. Stevens-Johnson syndrome (SJS) always involves mucosal surfaces but the skin involvement is limited by definition to 30% BSA. An intermediate form is recognised in which mucosal involvement is accompanied by skin involvement of 10-30% BSA (SJS-TEN overlap syndrome). All forms result in extensive sloughing and ulceration and carry a significant risk of fatal outcome.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code EB13 contains 4 clarifying diagnoses:

1. EB13.0 — Stevens-Johnson syndrome
   It contains 1 clarifying diagnosis.
2. EB13.1 — Toxic epidermal necrolysis
   It contains 1 clarifying diagnosis.
3. EB13.2 — Stevens-Johnson and toxic epidermal necrolysis overlap syndrome
   It contains 1 clarifying diagnosis.
4. EH63 — Stevens-Johnson syndrome and toxic epidermal necrolysis due to drug
   It contains 3 clarifying diagnoses.