ICD-11 classes
14 Diseases of the skin
Inflammatory dermatoses
Inflammatory erythemas and other reactive inflammatory...
EB13 — Stevens-Johnson syndrome or toxic epidermal necrolysis
EB13.1 — Toxic epidermal necrolysis

ICD-11 EB13.1 — Toxic epidermal necrolysis

Toxic epidermal necrolysis (TEN) is an acute life-threatening skin disease with commonly quoted overall risk of mortality of between 25 and 30%, though the risk of fatal outcome is around 90% in the most severely affected patients (SCORTEN score >5). It is characterised by the rapid onset of extensive erythema, necrosis, and bullous detachment of the epidermis (> 30% body surface area). Commonly, the mucous membranes are also involved. Death may result from a combination of sepsis, fluid depletion and multi-organ failure. In two thirds of cases, TEN is triggered by a clearly identifiable drug allergy.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code EB13.1 contains 1 clarifying diagnosis:

1. EH63.1 — Drug-induced toxic epidermal necrolysis