ICD-11 classes
13 Diseases of the digestive system
Diseases of liver
DB96 — Autoimmune liver disease

ICD-11 DB96 — Autoimmune liver disease

Autoimmune liver diseases are generally forms of chronic liver disease in which the etiology is unclear but autoimmune mechanisms are evident or postulated for the development of the disease. The primary target organ is the liver and/or biliary system. It can progress to liver cirrhosis.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code DB96 contains 5 clarifying diagnoses:

1. DB96.0 — Autoimmune hepatitis
2. DB96.1 — Primary biliary cholangitis
   It contains 3 clarifying diagnoses.
3. DB96.2 — Primary sclerosing cholangitis
   It contains 3 clarifying diagnoses.
4. DB96.Y — Other specified autoimmune liver disease
5. DB96.Z — Autoimmune liver disease, unspecified

The diagnosis is coded elsewhere:

• Organ specific autoimmune disorders #4082
• Autoimmune liver disease #4083