ICD-11 classes
13 Diseases of the digestive system
Diseases of liver
DB96 — Autoimmune liver disease
DB96.2 — Primary sclerosing cholangitis

ICD-11 DB96.2 — Primary sclerosing cholangitis

Primary sclerosing cholangitis is a chronic disease which shows focal or multifocal strictures of intra- and/or extra-hepatic bile ducts without any apparent causes, leading to cholestasis and ultimately liver cirrhosis and liver failure.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code DB96.2 contains 3 clarifying diagnoses:

1. DB96.20 — Primary sclerosing cholangitis with cirrhosis
2. DB96.2Y — Other specified primary sclerosing cholangitis
3. DB96.2Z — Primary sclerosing cholangitis, unspecified

The diagnosis is coded elsewhere:

• Autoimmune liver disease #4083
• Primary sclerosing cholangitis #4089