ICD-11 classes
04 Diseases of the immune system
Organ specific autoimmune disorders
DB96 — Autoimmune liver disease
DB96.2 — Primary sclerosing cholangitis
ICD-11 DB96.2 — Primary sclerosing cholangitis
Primary sclerosing cholangitis is a chronic disease which shows focal or multifocal strictures of intra- and/or extra-hepatic bile ducts without any apparent causes, leading to cholestasis and ultimately liver cirrhosis and liver failure.
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code DB96.2 contains 3 clarifying diagnoses:
- DB96.20 — Primary sclerosing cholangitis with cirrhosis
- DB96.2Y — Other specified primary sclerosing cholangitis
- DB96.2Z — Primary sclerosing cholangitis, unspecified
The diagnosis is coded elsewhere:
- Autoimmune liver disease #14319
- Primary sclerosing cholangitis #14325