ICD-11 classes
13 Diseases of the digestive system
Diseases of liver
5C90 — Metabolic or transporter liver disease

ICD-11 5C90 — Metabolic or transporter liver disease

The diagnosis has no description.

The diagnosis includes nothing.

Diagnosis with code 5C90 contains 16 clarifying diagnoses:

1. 5C90.0 — Liver diseases due to urea cycle defects
   It contains 3 clarifying diagnoses.
2. 5C90.1 — Liver diseases due to disorders of porphyrin or bilirubin metabolism or transport
   It contains 5 clarifying diagnoses.
3. 5C90.2 — Liver diseases due to disorders of amino acid metabolism
   It contains 2 clarifying diagnoses.
4. 5C90.3 — Liver disease due to disorders of lysosomal storage
5. 5C90.4 — Liver diseases due to mitochondrial disorders
6. 5C90.5 — Liver diseases due to disorders of mineral metabolism
   It contains 1 clarifying diagnosis.
7. 5C52.11 — Bile acid synthesis defect with cholestasis
8. 5C58.03 — Progressive familial intrahepatic cholestasis
9. 5C58.04 — Benign recurrent intrahepatic cholestasis
10. 5C51.3 — Glycogen storage disease
11. 5C51.4 — Disorders of galactose metabolism
    It contains 5 clarifying diagnoses.
12. 5C51.5 — Disorders of fructose metabolism
    It contains 4 clarifying diagnoses.
13. 5C5A — Alpha-1-antitrypsin deficiency
14. 8E46 — Reye syndrome
15. 5C90.Y — Other specified metabolic or transporter liver disease
16. 5C90.Z — Metabolic or transporter liver disease, unspecified

The diagnosis is coded elsewhere:

• Metabolic disorders #4709
• Metabolic or transporter liver disease #5084