ICD-11 classes
13 Diseases of the digestive system
Diseases of liver
5C90 — Metabolic or transporter liver disease
5C90.3 — Liver disease due to disorders of lysosomal storage
ICD-11 5C90.3 — Liver disease due to disorders of lysosomal storage
This is liver disease due to a group of approximately 50 rare inherited metabolic disorders that result from defects in lysosomal function.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
The diagnosis is included in 4 other classes.
- Gaucher disease (5C56.0Y)
- Niemann-Pick disease (5C56.0Y)
- Wolman disease (5C56.0Y)
- Cholesteryl ester storage disease (5C56.0Y)