ICD-11 classes
14 Diseases of the skin
Inflammatory dermatoses
Urticaria, angioedema and other urticarial disorders

ICD-11 Urticaria, angioedema and other urticarial disorders

A heterogeneous group of disorders characterised by dermal and/or subcutaneous and submucosal oedema. The most common underlying mechanism is release of histamine from mast cells with consequent capillary dilatation and tissue oedema. This is responsible for the weals of spontaneous and most physical urticarias. A variety of other mechanisms are involved in other urticarial disorders.

The diagnosis includes nothing.

It excludes 2 items.

  • Urticaria pigmentosa (2A21.10)
  • Papular urticaria (EK50.00)

Diagnosis contains 12 clarifying diagnoses:

  1. EB00 — Spontaneous urticaria
    It contains 2 clarifying diagnoses.
  2. EB01 — Inducible urticaria and angioedema
    It contains 5 clarifying diagnoses.
  3. EB02 — Cholinergic urticaria and related conditions
    It contains 3 clarifying diagnoses.
  4. EB03 — Syndromes with urticarial reactions or angioedema
    It contains 2 clarifying diagnoses.
  5. EB04 — Idiopathic angioedema
  6. EB05 — Urticaria of unspecified type
  7. 4A00.14 — Hereditary angioedema
  8. 4A00.15 — Acquired angioedema
  9. EF40.10 — Urticarial vasculitis
    It contains 1 clarifying diagnosis.
  10. 4A85.21 — Food-induced urticaria or angioedema
  11. EH61 — Drug-induced urticaria, angioedema and anaphylaxis
    It contains 3 clarifying diagnoses.
  12. EB0Y — Other specified urticarial disorders

The diagnosis is coded elsewhere:

The diagnosis is included in 6 other classes.

  • Hereditary angioedema (4A00.14)
  • Acquired angioedema (4A00.15)
  • Urticarial vasculitis (EF40.10)
  • Food-induced urticaria or angioedema (4A85.21)
  • Drug-induced urticaria, angioedema and anaphylaxis (EH61)
  • Angioedema due to disordered complement activation or kinin metabolism (4A00.1Y)

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