ICD-11 classes
14 Diseases of the skin
Inflammatory dermatoses
Urticaria, angioedema and other urticarial disorders
EF40.10 — Urticarial vasculitis

ICD-11 EF40.10 — Urticarial vasculitis

An uncommon form of cutaneous leucocytoclastic vasculitis manifested by urticarial weals which, in contrast to those of chronic urticaria, are long-lasting and painful rather than itchy. A cause is often not identified. It may be associated with hypocomplementaemia and systemic inflammation (hypocomplementaemic urticarial vasculitis).

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code EF40.10 contains 1 clarifying diagnosis:

  1. 4A44.91 — Hypocomplementaemic urticarial vasculitis

The diagnosis is coded elsewhere:

The diagnosis is included in 1 another class.

  • Hypocomplementaemic urticarial vasculitis (4A44.91)

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