ICD-11 classes
14 Diseases of the skin
Inflammatory dermatoses
Nonorgan specific systemic autoimmune disorders involving...
4A42 — Systemic sclerosis
4A42.0 — Paediatric onset systemic sclerosis

ICD-11 4A42.0 — Paediatric onset systemic sclerosis

Systemic sclerosis arising before the age of 16. Involvement of internal organs is less common but arthritis and myositis are more common than in adults.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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