ICD-11 classes
14 Diseases of the skin
Inflammatory dermatoses
Nonorgan specific systemic autoimmune disorders involving...
4A43 — Overlap or undifferentiated nonorgan specific systemic...
4A43.4 — Diffuse eosinophilic fasciitis
ICD-11 4A43.4 — Diffuse eosinophilic fasciitis
Also called Shulman disease/diffuse fasciitis, diffuse eosinophilic fasciitis is a rare idiopathic disorder associated with induration of the skin (orange-peel sign) that generally develops rapidly. It is a dermal and hypodermal sclerosis associated with fibrotic thickening of the subcutaneous adipose lobular septa, superficial fascia, and perimysium. Full thickness excisional biopsy of skin lesions revealing fibrosis of the subcutaneous fascia is generally required for diagnosis. Onset follows unusual physical exertion and trauma, especially in males.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: