ICD-11 classes
14 Diseases of the skin
Inflammatory dermatoses
Autoinflammatory disorders
4A60 — Monogenic autoinflammatory syndromes
4A60.2 — Tumour necrosis factor receptor 1 associated periodic...
ICD-11 4A60.2 — Tumour necrosis factor receptor 1 associated periodic syndrome
TRAPS is an autoinflammatory disease associated with heterozygous mutations in the gene coding for tumour necrosis factor (TNF) receptor 1 (TNFR1).This results in clinical attacks of inflammation in the form of fever and serositis in the form of peritoneal, pleural or synovial inflammation along with increased acute phase reactants.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: