ICD-11 classes
14 Diseases of the skin
Genetic and developmental disorders affecting the skin
EC20 — Genetic disorders of keratinisation

ICD-11 EC20 — Genetic disorders of keratinisation

Heritable disorders characterised by abnormal epidermal keratinization. They include the ichthyoses and palmoplantar keratodermas.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code EC20 contains 7 clarifying diagnoses:

1. EC20.0 — Non-syndromic ichthyosis
   It contains 5 clarifying diagnoses.
2. EC20.1 — Hereditary skin peeling
3. EC20.2 — Hereditary acantholytic dermatoses
4. EC20.3 — Hereditary palmoplantar keratodermas
   It contains 4 clarifying diagnoses.
5. LD27.2 — Syndromic ichthyosis
   It contains 1 clarifying diagnosis.
6. ED56 — Keratosis pilaris
7. EC20.Y — Other specified genetic disorders of keratinisation