ICD-11 classes
14 Diseases of the skin
Genetic and developmental disorders affecting the skin
EC20 — Genetic disorders of keratinisation
EC20.2 — Hereditary acantholytic dermatoses
ICD-11 EC20.2 — Hereditary acantholytic dermatoses
A group of heritable disorders characterised by epidermal acantholysis and loss of epidermal integrity.
It includes 2 items.
- Darier disease
- Hailey-Hailey disease
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: