ICD-11 classes
14 Diseases of the skin
Skin disorders involving specific cutaneous structures
Disorders of the epidermis and epidermal appendages
Disorders of epidermal keratinisation
ED55 — Palmoplantar keratodermas
EC20.3 — Hereditary palmoplantar keratodermas
EC20.30 — Diffuse palmoplantar keratodermas
LD27.03 — Hidrotic ectodermal dysplasia, Clouston type
ICD-11 LD27.03 — Hidrotic ectodermal dysplasia, Clouston type
Clouston syndrome (or hidrotic ectodermal dysplasia) is an inherited disorder characterised by the clinical triad of nail dystrophy, alopecia, and palmoplantar hyperkeratosis.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Ectodermal dysplasia syndromes #15941
- Diffuse palmoplantar keratodermas #15961
- Genetic syndromes with alopecia or hypotrichosis #15975
- Genetic syndromes affecting nails #15983
- Genetic syndromes with alopecia or hypotrichosis #16341
- Genetic syndromes affecting nails #16460
- Ectodermal dysplasia syndromes #23325
- Genetic syndromes affecting nails #23337