ICD-11 classes
14 Diseases of the skin
Skin disorders involving specific cutaneous structures
Disorders of the dermis and subcutis
Disorders of cutaneous connective tissue
Genetic disorders affecting dermal collagen, elastin or...
LD28.1 — Ehlers-Danlos syndrome
ICD-11 LD28.1 — Ehlers-Danlos syndrome
Ehlers – Danlos syndrome (EDS) is a heterogeneous group of inherited disorders of connective tissue, principally collagen, that range in severity from mild joint hypermobility to life-threatening fragility of soft tissue and vasculature.
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code LD28.1 contains 2 clarifying diagnoses:
- LD28.10 — Ehlers-Danlos syndrome, classical type
- LD28.1Y — Other specified types of Ehlers-Danlos syndrome
The diagnosis is coded elsewhere:
- Genetic disorders affecting dermal collagen, elastin or other matrix proteins #16008
- Ehlers-Danlos syndrome #16010
- Syndromes with connective tissue involvement as a major feature #18723
- Ehlers-Danlos syndrome #18729
- Syndromes with connective tissue involvement as a major feature #23364
- Ehlers-Danlos syndrome #23370