ICD-11 classes
20 Developmental anomalies
Multiple developmental anomalies or syndromes
LD28 — Syndromes with connective tissue involvement as a major...
LD28.1 — Ehlers-Danlos syndrome
ICD-11 LD28.1 — Ehlers-Danlos syndrome
Ehlers – Danlos syndrome (EDS) is a heterogeneous group of inherited disorders of connective tissue, principally collagen, that range in severity from mild joint hypermobility to life-threatening fragility of soft tissue and vasculature.
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code LD28.1 contains 2 clarifying diagnoses:
- LD28.10 — Ehlers-Danlos syndrome, classical type
- LD28.1Y — Other specified types of Ehlers-Danlos syndrome
The diagnosis is coded elsewhere:
- Genetic disorders affecting dermal collagen, elastin or other matrix proteins #16008
- Ehlers-Danlos syndrome #16010
- Genetic disorders affecting dermal collagen, elastin or other matrix proteins #16515
- Ehlers-Danlos syndrome #16517
- Syndromes with connective tissue involvement as a major feature #18723
- Ehlers-Danlos syndrome #18729