ICD-11 classes
14 Diseases of the skin
Skin disorders involving specific cutaneous structures
Disorders of cutaneous blood and lymphatic vessels
Malformations involving cutaneous lymphatic vessels
LA90.1 — Lymphatic malformations
BD93.0 — Primary lymphoedema
EE11.1 — Yellow nail syndrome
ICD-11 EE11.1 — Yellow nail syndrome
Yellow nail syndrome is characterised by yellow, dystrophic, thick and slowly growing nails, associated with lymphoedema and respiratory involvement. Less than 100 cases have been described. Lymphoedema occurs more often in the lower limbs. It can appear at birth or later in life. Onset generally follows the onset of ungual abnormalities. Patients usually suffer from chronic bronchitis and in some cases, from chronic sinusitis, bronchiectasia and recurring pneumonitis. They can also present with pleural effusion (30% of cases) and bronchial hyperreactivity. Most cases are sporadic. However, familial forms have been described. Aetiology is unknown.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Primary lymphoedema #11642
- Primary lymphoedema #11664
- Primary lymphoedema #12174
- Pulmonary lymphatic dysplasia syndromes #12745
- Acquired abnormalities of nail colour #16434
- Primary lymphoedema #16697
- Cutaneous markers of internal disorders #17427
- Primary lymphoedema #22708
- Primary lymphoedema #23223