ICD-11 classes
02 Neoplasms
Neoplasms of haematopoietic or lymphoid tissues
2B32 — Immunodeficiency-associated lymphoproliferative disorders

ICD-11 2B32 — Immunodeficiency-associated lymphoproliferative disorders

Post-transplant lymphoproliferative disorder (PTLD) is a polyclonal (benign) or clonal (malignant) proliferation of lymphoid cells that develops as a consequence of immunosuppression in a recipient of a solid organ or bone marrow allograft. PTLDs comprise a spectrum ranging from early, Epstein-Barr virus (EBV)-driven polyclonal lymphoid proliferations to EBV-positive or EBV- negative lymphomas of predominantly B-cell or less often T-cell type. In other Immunodeficiency-associated lymphoproliferative disorders, association with EBV is less pronounced.

It includes 1 item.

  • PTLD - [Post transplant lymphoproliferative disorder]

The diagnosis excludes nothing.

Diagnosis with code 2B32 contains 6 clarifying diagnoses:

  1. 2B32.0 — Post-transplant lymphoproliferative disorder, early lesion
  2. 2B32.1 — Reactive plasmacytic hyperplasia
  3. 2B32.2 — Post-transplant lymphoproliferative disorder, Infectious mononucleosis-like
  4. 2B32.3 — Polymorphic post-transplant lymphoproliferative disorder
  5. 2B32.Y — Other specified immunodeficiency-associated lymphoproliferative disorders
  6. 2B32.Z — Immunodeficiency-associated lymphoproliferative disorders, unspecified

The diagnosis is coded elsewhere:

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