ICD-11 classes
03 Diseases of the blood or blood-forming organs
Neoplasms of haematopoietic or lymphoid tissues

ICD-11 Neoplasms of haematopoietic or lymphoid tissues

A neoplasm arising from hematopoietic cells found in the bone marrow, peripheral blood, lymph nodes and spleen (organs of the hematopoietic system). Hematopoietic cell neoplasms can also involve other anatomic sites (e.g. central nervous system, gastrointestinal tract), either by haematogenous spread, direct tumour infiltration, or neoplastic transformation of extranodal lymphoid tissues. The commonest forms are the various types of leukaemia, Hodgkin and non-Hodgkin lymphomas, myeloproliferative neoplasms and myelodysplastic syndromes.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis contains 15 clarifying diagnoses:

1. Myeloproliferative neoplasms
   It contains 3 clarifying diagnoses.
2. Myelodysplastic syndromes
   It contains 11 clarifying diagnoses.
3. Myelodysplastic and myeloproliferative neoplasms
   It contains 7 clarifying diagnoses.
4. Myeloid and lymphoid neoplasms with eosinophilia and abnormalities of PDGFRA, PDGFRB or FGFR1
   It contains 4 clarifying diagnoses.
5. 2A60 — Acute myeloid leukaemias and related precursor neoplasms
   It contains 8 clarifying diagnoses.
6. 2A61 — Acute leukaemias of ambiguous lineage
7. Precursor lymphoid neoplasms
   It contains 3 clarifying diagnoses.
8. Mature B-cell neoplasms
   It contains 8 clarifying diagnoses.
9. Mature T-cell or NK-cell neoplasms
   It contains 4 clarifying diagnoses.
10. 2B30 — Hodgkin lymphoma
    It contains 3 clarifying diagnoses.
11. 2B31 — Histiocytic or dendritic cell neoplasms
    It contains 10 clarifying diagnoses.
12. 2B32 — Immunodeficiency-associated lymphoproliferative disorders
    It contains 6 clarifying diagnoses.
13. 2B33 — Malignant haematopoietic neoplasms without further specification
    It contains 7 clarifying diagnoses.
14. Symptoms of blood, blood-forming organs, or the immune system
    It contains 4 clarifying diagnoses.
15. 2B3Z — Neoplasms of haematopoietic or lymphoid tissues, unspecified

The diagnosis is coded elsewhere:

• 02 Neoplasms #1491
• Neoplasms of haematopoietic or lymphoid tissues #1534