ICD-11 classes
03 Diseases of the blood or blood-forming organs
Neoplasms of haematopoietic or lymphoid tissues
Myelodysplastic syndromes

ICD-11 Myelodysplastic syndromes

Clonal hematopoietic disorders characterised by dysplasia and ineffective hematopoiesis in one or more of the hematopoietic cell lines. The dysplasia may be accompanied by an increase in myeloblasts, but the number is less than 20% in marrow and blood, which, according to the WHO guidelines, is the requisite threshold for the diagnosis of acute myeloid leukaemia.

The diagnosis includes nothing.

Diagnosis contains 11 clarifying diagnoses:

1. 2A30 — Refractory anaemia
2. 2A31 — Refractory neutropaenia
3. 2A32 — Refractory thrombocytopenia
4. 2A33 — Refractory anaemia with ring sideroblasts
5. 2A34 — Refractory cytopenia with multi-lineage dysplasia
6. 2A35 — Refractory anaemia with excess of blasts
7. 2A36 — Myelodysplastic syndrome with isolated del(5q)
8. 2A37 — Myelodysplastic syndrome, unclassifiable
9. 2A38 — Refractory cytopenia of childhood
10. 2A3Y — Other specified myelodysplastic syndromes
11. 2A3Z — Myelodysplastic syndromes, unspecified

The diagnosis is coded elsewhere:

• Neoplasms of haematopoietic or lymphoid tissues #1534
• Myelodysplastic syndromes #1568