ICD-11 classes
03 Diseases of the blood or blood-forming organs
Neoplasms of haematopoietic or lymphoid tissues
Myelodysplastic and myeloproliferative neoplasms

ICD-11 Myelodysplastic and myeloproliferative neoplasms

A category of clonal haematopoietic disorders that have both myelodysplastic and myeloproliferative features at the time of initial presentation.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis contains 7 clarifying diagnoses:

1. 2A40 — Chronic myelomonocytic leukaemia
2. 2A41 — Atypical chronic myeloid leukaemia, BCR-ABL1- negative
3. 2A42 — Juvenile myelomonocytic leukaemia
   It contains 3 clarifying diagnoses.
4. 2A43 — Refractory anaemia with ring sideroblasts associated with marked thrombocytosis
5. 2A44 — Myeloproliferative and myelodysplastic disease, unclassifiable
6. 2A4Y — Other specified myelodysplastic and myeloproliferative neoplasms
7. 2A4Z — Myelodysplastic and myeloproliferative neoplasms, unspecified

The diagnosis is coded elsewhere:

• Neoplasms of haematopoietic or lymphoid tissues #1534
• Myelodysplastic and myeloproliferative neoplasms #1580