ICD-11 classes
03 Diseases of the blood or blood-forming organs
Neoplasms of haematopoietic or lymphoid tissues
Myelodysplastic and myeloproliferative neoplasms
2A42 — Juvenile myelomonocytic leukaemia
ICD-11 2A42 — Juvenile myelomonocytic leukaemia
A myelodysplastic/myeloproliferative neoplasm of childhood that is characterised by proliferation principally of the granulocytic and monocytic lineages. Myelomonocytic proliferation is seen in the bone marrow and the blood. The leukemic cells may infiltrate any tissue, however liver, spleen, lymph nodes, skin, and respiratory tract are the most common sites of involvement.
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code 2A42 contains 3 clarifying diagnoses:
- 2A42.0 — Juvenile myelomonocytic leukaemia in complete remission
- 2A42.Y — Other specified juvenile myelomonocytic leukaemia
- 2A42.Z — Juvenile myelomonocytic leukaemia, unspecified
The diagnosis is coded elsewhere: