ICD-11 classes
15 Diseases of the musculoskeletal system or connective...
Nonorgan specific systemic autoimmune disorders
4A41 — Idiopathic inflammatory myopathy
4A41.2 — Inclusion body myopathy

ICD-11 4A41.2 — Inclusion body myopathy

Inclusion body myopathy (IBM) is distinguished from polymyositis (PM) and dermatomyositis (DM) on the basis of clinical and histopathological features. A characteristic clinical phenotype is characterised by insidious onset of muscle weakness over months to years, muscle weakness localised predominantly in the thigh muscles and finger flexors, and resistance to glucocorticoid treatment. Typical histopathologic features include sarcoplasmic and nuclear inclusions and rimmed vacuoles. (Kelley's Textbook of Rheumatology, 6th Ed.)

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 4A41.2 contains 3 clarifying diagnoses:

  1. 4A41.20 — Inflammatory inclusion body myositis
  2. 4A41.21 — Noninflammatory inclusion body myopathy
  3. 4A41.2Z — Inclusion body myopathy, unspecified

The diagnosis is coded elsewhere:

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