ICD-11 classes
08 Diseases of the nervous system
Diseases of neuromuscular junction or muscle
Primary disorders of muscles
4A41 — Idiopathic inflammatory myopathy

ICD-11 4A41 — Idiopathic inflammatory myopathy

These comprise a diverse group of syndromes that have in common persistent muscle inflammation of unknown pathophysiology, resulting in damage that affects muscle function. The inflammatory muscle disease can either be acute or chronic in nature.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 4A41 contains 5 clarifying diagnoses:

1. 4A41.0 — Dermatomyositis
   It contains 3 clarifying diagnoses.
2. 4A41.1 — Polymyositis
   It contains 4 clarifying diagnoses.
3. 4A41.2 — Inclusion body myopathy
   It contains 3 clarifying diagnoses.
4. 4A41.Y — Other specified idiopathic inflammatory myopathy
5. 4A41.Z — Idiopathic inflammatory myopathy, unspecified

The diagnosis is coded elsewhere:

• Nonorgan specific systemic autoimmune disorders #3617
• Idiopathic inflammatory myopathy #3631
• Primary disorders of muscles #10017
• Idiopathic inflammatory myopathy #10073
• Nonorgan specific systemic autoimmune disorders #18345
• Idiopathic inflammatory myopathy #18359